Treatment for the hearing loss may include hearing aids or surgery for a cochlear implant. All three types are inherited in an autosomal recessive manner. The different types are distinguished by their severity and the age when signs and symptoms appear. In some cases, vision is further impaired by clouding of the lens of the eye ( cataracts ). Three major types of Usher syndrome have been described - types I, II, and III. Night vision loss begins first, followed by blind spots that develop in the side (peripheral) vision, that can enlarge and merge to produce tunnel vision (loss of all peripheral vision). Vision loss occurs as the light-sensing cells of the retina gradually deteriorate. Retinitis pigmentosa is an eye disease that affects the layer of light-sensitive tissue at the back of the eye ( the retina ). Sensorineural hearing means it is caused by abnormalities of the inner ear. Listen Usher syndrome is a genetic disorder characterized by sensorineural hearing loss or deafness and progressive vision loss due to retinitis pigmentosa. Table of Contents expand submenu for Table of Contents.Preguntas Más Frecuentes Sobre los Trastornos Cromosómicos.Consejos Para Obtener Ayuda Financiera Para Una Enfermedad.Consejos Para una Condición no Diagnosticada.Como Encontrar un Especialista en su Enfermedad.
Preguntas Más Frecuentes Sobre Enfermedades Raras.Guías de Información expand submenu for Guías de Información.En Español expand submenu for En Español.About GARD expand submenu for About GARD.Teachers and Students expand submenu for Teachers and Students.Researchers expand submenu for Researchers.Caring for Your Patient with a Rare Disease.Healthcare Professionals expand submenu for Healthcare Professionals.Children with type 3 Usher syndrome often develop hearing loss by adolescence, requiring hearing aids by mid-to-late adulthood. Most have normal to near-normal balance, but some develop balance problems with age. Patients, Families and Friends expand submenu for Patients, Families and Friends Type 3: Children with type 3 Usher syndrome have normal hearing at birth.Find Diseases By Category expand submenu for Find Diseases By Category.